Tumor Information / Malignant Soft Tissue Tumors
>> Malignant Soft Tissue Tumors  

Dermatofibrosarcoma Protuberans (DFSP)

  • Age distribution: early/mid-adulthood, male predominance
  • Presentation: starts as plaque-like lesion initially and progresses to protuberant multinodular mass, metastases relatively rare
  • Location: cutaneous, trunk and proximal extremities
  • Treatment: Wide resection

 

Malignant Fibrous Histiocytoma (MFH)

  • Age distribution: 50-70 years old, male:female ratio = 2:1, most common soft tissue sarcoma
  • Presentation: painless, enlarging mass
  • Location: most common location is thigh
  • Treatment: wide excision, possible chemotherapy and radiation

 

Liposarcoma

  • Age distribution: average age 57, second most common soft tissue sarcoma, male:female ratio = 3:2
  • Location: Most common in the thigh, retroperitoneum and inguinal areas
  • Treatment: wide excision, possible chemotherapy and radiation

 

Synovial sarcoma

  • Age distribution: average age 35, third most common soft tissue sarcoma
  • Presentation: mass but can be associated with pain, does not arise from synovial tissue but may be near joints, soft tissue tumor most likely to demonstrate mineralization
  • Treatment: wide excision, possible chemotherapy and radiation